Diagnostics and surgical treatment of Hirsprung disease in newborns and patients in the first months of life
https://doi.org/10.51922/1818-426X.2022.2.4
Abstract
The lack of a unified methodological approach to the treatment of newborns with Hirschsprung's disease in medical institutions of the country, non-standardized diagnostic and surgical treatment programs lead to late detection of the disease and, accordingly, late surgical treatment. Therefore, one of the important principles of organizing the work of specialists from various services is mutual continuity and understanding at each stage of work.
Aim. Analysis of diagnostics and principles of surgical treatment of patients in the first months of life with Hirschsprung's disease. From 2010 to 2019, diagnostics (X-ray and morphological examinations) were carried out at the Republican Scientific and Practical Center for Pediatric Surgery in 51 newborn patients in whom Hirschsprung's disease was confirmed. The patients were divided into 2 groups with uncomplicated and complicated course of the disease: uncomplicated form – 36 patients with persistent constipation, 32 of whom were radically operated on before the age of 3 months; complicated form – 15 patients who had a stoma removed due to intestinal obstruction, peritonitis or necrotizing enterocolitis.
About the Authors
O. A. GovorukhinaBelarus
N. S. Prokopenya
Belarus
V. A. Kharitonchik
Belarus
V. M. Khomich
Belarus
References
1. Kotin, A. N., Arintsina I. A., Bairov V. G., Dreyyer K. L., Karavayeva S. A., Nemilova T. K., Popov A. A. Khirurgicheskaya taktika pri bolezni Girshprunga u novorozhdennykh // [Surgical tactics for Hirschsprung’s disease in newborns] Surgery. – 1993. – № 8. – S. 44–49.
2. Friedmacher, F., Puri P. Classification and diagnostic criteria of variants of Hirschsprung’s disease // Pediatric surgery international. – 2013. – Т. 29, № 9. – P. 855–872.
3. Holschneider, A. M., Puri P. eds. Hirschsprung’s Disease and Allied Disorders. 3rd ed. – New York: Springer, 2008. – 414 p.
4. Kapur, R. P., Reed R. C., Finn L. S., Patterson K., Johanson J., Rutledge J. C. Calretinin immunohistochemistry versus acetylcholinesterase histochemistry in the evaluation of suction rectal biopsies for Hirschsprung disease // Pediatr. Dev. Pathol. – 2009. – № 12. – P. 6–15.
5. De la Torre, L., Ortega-Salgado J. A. Transanal endorectal pull-through for Hirschsprung’s disease // J. Pediatr. Surg. – 1998. – № 33. – Р. 1283–1286.
6. Georgeson, K. E., Robertson D. J. Laparoscopic-assisted approaches for the definitive surgery for Hirschsprung’s disease // Semin Pediatr Surg. – 2004. – № 13. – Р. 256–62.
7. Zani, A., Eaton S., Morini F., Puri P., Rintala R., Van Heurn E. EUPSA Network Office (2016). European Paediatric Surgeons’ Association Survey on the Management of Hirschsprung Disease // Eur. J. Pediatr. Surg. – 2012. – № 1. – Р. 96–101.
Review
For citations:
Govorukhina O.A., Prokopenya N.S., Kharitonchik V.A., Khomich V.M. Diagnostics and surgical treatment of Hirsprung disease in newborns and patients in the first months of life. Medical Journal. 2022;(2):4-11. (In Russ.) https://doi.org/10.51922/1818-426X.2022.2.4